Table 2 Summary of published CLIPPERS case reports; initial- and follow up therapy

Pittock et al. [1]

8

4

prednisone

1 patient: prednisone and methotrexate

144

no

6/8

1 patient: prednisone

25 (died)

no

1 patient: prednisone and azathioprine

43

no

1 patient: prednisone and mitoxantrone

14

no

4 patients: prednisone

20, 7, 22 and 7

no

Simon et al. [2]

5

5

prednisone

1 patient: prednisone and methotrexate

12

no

5/5

2 patients: prednisone, azathioprine and cylophosphamide

36, 72

no

1 patient: prednisone, mycophenolate and cylophosphamide

64

no

1 patient: prednisone and cylophosphamide

100

no

Taieb et al. [3]

1

1

prednisone

prednisone and rituximab

9

no

unknown

Jones et al. [4]

2*

1*

prednisone

prednisone

> 6

no

1/1

Sempere et al. [5]

1

-

prednisone

prednisone and methotrexate

6

no

unknown

Duprez et al. [6]

1

-

prednisone

unknown

> 3

unknown

unknown

List et al. [7]

1

-

prednisone

prednisone and methotrexate

> 3

no

unknown

Limousin et al. [8]

1**

1**

-

-

-

-

-

Gabilondo et al.[9]

1

-

prednisone

prednisone, immunoglobulins iv once and azathioprine

9

no

1/1

Kastrup et al. [10]

3

3

2/3 prednisone

1 patient: prednisone and cyclophosphamide

17

no

3/3

1 patient: prednisone

15

no

1/3 dexamethason

1 patient: dexamethason and methotrexate

9

no

Biotti et al. [11]

1

-

prednisone

prednisone and azathioprine

7

no

unknown