From: Need for prolonged immunosupressive therapy in CLIPPERS-a case report
Author | Cases | Biopsy | Initial treatment | Maintenance treatment | Follow up (months) | Therapy stopped | Decline*** |
---|---|---|---|---|---|---|---|
Pittock et al. [1] | 8 | 4 | prednisone | 1 patient: prednisone and methotrexate | 144 | no | 6/8 |
1 patient: prednisone | 25 (died) | no | |||||
1 patient: prednisone and azathioprine | 43 | no | |||||
1 patient: prednisone and mitoxantrone | 14 | no | |||||
4 patients: prednisone | 20, 7, 22 and 7 | no | |||||
Simon et al. [2] | 5 | 5 | prednisone | 1 patient: prednisone and methotrexate | 12 | no | 5/5 |
2 patients: prednisone, azathioprine and cylophosphamide | 36, 72 | no | |||||
1 patient: prednisone, mycophenolate and cylophosphamide | 64 | no | |||||
1 patient: prednisone and cylophosphamide | 100 | no | |||||
Taieb et al. [3] | 1 | 1 | prednisone | prednisone and rituximab | 9 | no | unknown |
Jones et al. [4] | 2* | 1* | prednisone | prednisone | > 6 | no | 1/1 |
Sempere et al. [5] | 1 | - | prednisone | prednisone and methotrexate | 6 | no | unknown |
Duprez et al. [6] | 1 | - | prednisone | unknown | > 3 | unknown | unknown |
List et al. [7] | 1 | - | prednisone | prednisone and methotrexate | > 3 | no | unknown |
Limousin et al. [8] | 1** | 1** | - | - | - | - | - |
Gabilondo et al.[9] | 1 | - | prednisone | prednisone, immunoglobulins iv once and azathioprine | 9 | no | 1/1 |
Kastrup et al. [10] | 3 | 3 | 2/3 prednisone | 1 patient: prednisone and cyclophosphamide | 17 | no | 3/3 |
1 patient: prednisone | 15 | no | |||||
1/3 dexamethason | 1 patient: dexamethason and methotrexate | 9 | no | ||||
Biotti et al. [11] | 1 | - | prednisone | prednisone and azathioprine | 7 | no | unknown |