From: Clinical analysis of adult-onset spinocerebellar ataxias in Thailand
Factors | SARA ≥15 N = 49 (%) | SARA <15 N = 34 (%) | p-value |
---|---|---|---|
Sex | Â | Â | Â |
 Female | 23 (46.9) | 14 (41.2) | 0.603 |
Age onset (years); mean (SD) | 42.1 (11.1) | 37.5 (11.3) | 0.071 |
Age when exam (years); mean (SD) | 50.5 (11.7) | 39.5 (11.3) | <0.001 |
Duration (years); mean (SD) | 8.9 (5.1) | 3.4 (2.2) | <0.0001 |
SCA Type | Â | Â | Â |
 SCA 1 | 13 (26.5) | 8 (23.5) | 0.325 |
 SCA 2 | 6 (12.2) | 9 (26.5) |  |
 SCA 3 | 26 (53.1) | 13 (38.2) |  |
 SCA 6 | 4 (8.2) | 4 (11.8) |  |
Family history | 44 (89.8) | 24 (70.6) | 0.025 |
Slow saccades | 29 (59.2) | 14 (41.2) | 0.106 |
Horizontal nystagmus | 32 (65.3) | 17 (50) | 0.163 |
Vertical nystagmus | 8 (16.3) | 2 (5.9) | 0.187 |
Upward gaze paresis | 31 (63.3) | 6 (17.6) | <0.001 |
Hyperreflexia | 37 (75.5) | 20 (58.8) | 0.107 |
Areflexia | 10 (20.4) | 4 (11.8) | 0.301 |
Babinski’s sign | 26 (53.1) | 12 (35.3) | 0.110 |
Sensory impairment | 14 (28.6) | 2 (5.9) | 0.010 |
Optic atrophy | 4 (8.2) | 0 (0) | 0.141 |