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Table 1 Patient characteristics

From: In myotonic dystrophy type 1 reduced FDG-uptake on FDG-PET is most severe in Brodmann area 8

Patient Number

Sex

Age symptom onset

Age at FDG-PET

CTG expansion

Diabetes (glucose level)

1

F

58 (late onset)

64

83

No (<120 mg/dl)

2

M

35 (late onset)

74

100

No (<120 mg/dl)

3

F

45 (late onset)

64

150

Yes (120–160 mg/dl)

4

F

32 (late onset)

46

176

No (<120 mg/dl)

5

F

25 (late onset)

41

230

No (<120 mg/dl)

6

F

30 (late onset)

49

330

No (<120 mg/dl)

7

M

26 (late onset)

36

400

No (<120 mg/dl)

8

M

30 (late onset)

50

400

Yes (120–160 mg/dl)

9

F

19 (late onset)

26

400

No (<120 mg/dl)

10

F

30 (late onset)

49

400

No (<120 mg/dl)

11

M

40 (late onset)

58

430

No (<120 mg/dl)

12

F

14 (early onset)

34

660

No (<120 mg/dl)

13

F

13 (early onset)

27

660

No (<120 mg/dl)

14

F

14 (early onset)

31

670

No (<120 mg/dl)

15

F

28 (late onset)

54

850

Yes (120–160 mg/dl)

16

F

39 (late onset)

47

1000

No (<120 mg/dl)

17

M

40 (late onset)

51

1168

Yes (<120 mg/dl)

18

M

24 (late onset)

44

1300

No (<120 mg/dl)c

19

F

28 (late onset)

50

1400

No (<120 mg/dl)

20

M

29 (late onset)

46

1500

No (<120 mg/dl)

21

F

38 (late onset)

58

1560

No (<120 mg/dl)

22

M

5 (early onset)

41

1600

No (<120 mg/dl)

23

M

14 (early onset)

55

1700

Yes (<120 mg/dl)

24

F

6 (early onset)

26

2000

Yes (<120 mg/dl)