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Table 1 Electrophysiological studies of MADD in the two patients

From: Acute-onset multiple acyl-CoA dehydrogenase deficiency mimicking Guillain-Barré syndrome: two cases report

Motor nerve

Case 1

Case 2

MNCV(m/s)

dL (ms)

CMAP (mV)

MNCV(m/s)

dL (ms)

CMAP (mV)

L Median

E-W

74(≥50.0)

7.2(≥5.0)

54

13.0

W-APB

3.3(≤4.2)

8.5(≥5.0)

3.3

13.8

R Median

E-W

67

5.3

56

16.1

W-APB

3.4

5.8

3.0

16.9

L Ulnar

E-W

66(≥53.0)

7.6(≥5.5)

53

11.0

W-ADM

2.1(≤4.2)

9.5(≥5.5)

2.5

12.4

R Ulnar

E-W

68

8.1

61

10.7

W-ADM

2.0

8.5

2.2

11.0

L Peroneal

FH-A

47(≥38.0)

3.7(≥3.0)

43

2.6

A-EBD

3.0(≤6.1)

5.1(≥3.0)

3.8

3.3

R Peroneal

FH-A

58

10.3

50

3.3

A-EBD

3.7

12.5

4.6

3.7

L Tibial

PF-A

51(≥35.0)

12.0(≥3.0)

50

13.6

A-AA

4.8(≤6.1)

13.9(≥3.0)

4.8

165

R Tibial

PF-A

56

11.4

52

11.5

A-AA

4.4

11.2

5.3

12.8

Sensory nerve

SNCV (m/s)

SNAP (uV)

SNCV (m/s)

SNAP (uV)

L-Median

IIF-W

59(≥50.8)

14.4(≥8.0)

35

1.5

R-Median

IIF-W

57

11.9

48

1.1

L-Sural

A-SURA

42(≥41.9)

15.5(≥7.0)

NR

NR

R-Sural

A-SURA

45

26.3

NR

NR

F wave

F-Lat(ms)

F-Lat(ms)

L-Median

29.5(≤32.0)

27.31

R- Median

27.62

27.0

H Reflex

H-Lat(ms)

H-Lat(ms)

L Tibial

28.0(< 40.0)

32.89

R Tibial

28.0

31.26

  1. MNCV motor nerve conduction velocity, CMAP compound motor action potential, dL distal motor latency, SNCV sensory nerve conduction velocity, SNAP sensory nerve action potential, L left, R right, E elbow, W wrist, APB abductor pollicis brevis, ADM abductor digiti minimi, FH fibula head, A ankle, EDB extensor digitorum brevis, PF popliteal fossa, AA abductor allucis, IIF second finger, SURA sural, Lat latency, NR no recorded. Normal values are given in brackets