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Table 1 Predominant distribution of stiffness and other neurological signs in 57 patients with Stiff Person Syndrome

From: Quantitative clinical and autoimmune assessments in stiff person syndrome: evidence for a progressive disorder

Symptoms n (%)
Increased tone in:
 Face 16 (28)
 Cervical paraspinal and shoulder girdle muscles 11 (19)
 Thoracic paraspinal and abdominal wall muscles 14 (24)
 Lumbosacral paraspinal muscles 16 (28)
 Proximal leg muscles 17 (30)
 Combined lumbosacral paraspinal and proximal leg muscles 33 (58)
 Axial (diffuse paraspinal and proximal limb muscles) 39 (68)
 Asymmetry with one limb predominant (stiff-limb) 6 (10)
 Distal limb stiffness 4 (7)
Spasms 50 (88)
Other associated symptoms:
 Ocular symptoms 13 (23)
 Cerebellar symptoms and signs 7 (12)
Functional impairment resulting in the following:
 Stiff or impaired gait 54 (94)
 Hyperlordosis 48 (84)
 Shortness of breath 11 (19)
 Need for cane 26 (45)
 Need for walker 14 (24)
 Need for wheelchair 9 (15)
 Inability to work 48 (84)
 Startle response 55 (96)
 Anxiety and task-specific phobias 52 (91)
 Depressed mood 3 (5)