Table 1 Participants’ characteristics and mean and median ages; comparison of values along the analysed 10-year period by means of the Mann-Whitney U test

Number of patients

47

47

–

 Male

16

16

–

 Female

31

31

–

Age (years)

36.87 ± 12.50

47.21 ± 12.42

–

 Male

36.67 ± 9.90

46.81 ± 9.89

–

 Female

36.96 ± 13.81

47.45 ± 13.70

–

Age at onset (years)

1 [1.00; 2.00]

1 [1.00; 2.00]

–

Age of gait loss

10.00 [7.00; 15.00]

10.00 [7.00; 15.00]

–

Age of manual function loss

–

38.00 [20.00; 41.50]

–

Barthel Índice

39.00 [24.50; 51.50]

22.00 [18.00;33.50]

< 0.001^a

Grip strength R

3.00 [0.00; 9.00]

0.00 [0.00; 0.00]

< 0.001^a

Grip strength L

2.00 [0.00; 7.00]

0.00 [0.00; 0.00]

< 0.001^a

SPRS

40.50 [38.00;43.75]

41.00 [38.00;44.00]

0.195

Deluca

9.00 [8.00; 9.00]

9.00 [9.00;9.00]

0.982

Smith

1.00 [1.00; 2.00]

1.00 [1.00; 1.00]

0.257

Fink Scale

5.00 [4.0; 5.0]

5.00 [5.0; 5.0]

0.998