From: Taste disorder in facial onset sensory and motor neuronopathy: a case report
Patient | Age at onset, y/sex | Initial symptoms | Clinical course | Autoantibodies | Response to treatments | Reference |
---|---|---|---|---|---|---|
Present case | 49/M | Taste disorder | Weakness of the upper limbs at age of 55 Mechanical ventilation and tube feeding at age of 58 | (−) | No response to IVIG | |
1 | 42/M | Taste disorder Perioral paresthesia and numbness | Weakness of the neck and shoulder girdles at the age of 50 Tube feeding at the age of 51 Died at the age of 52 due to pulmonary embolism | (+), Anti-sulfatide antibody | No response to PDN, AZA and MMF | [10] |
2 | 63/F | Facial paresthesia | NA | (−) | A part of patients 2–8 were treated with IVIG, but none of them responded to the treatment. | [18] |
3 | 44/F | Facial paresthesia | NA | (−) | [18] | |
4 | 40/M | Dysarthria | NA | (−) | [18] | |
5 | 41/M | Facial paresthesia and weakness | NA | (−) | [18] | |
6 | 62/F | Facial paresthesia and weakness | NA | (−) | [18] | |
7 | 50/F | Facial and upper limbs’ paresthesia and weakness | NA | (−) | [18] | |
8 | 51/M | Facial paresthesia and weakness Weakness of upper limbs | NA | (−) | [18] |