Male sex, n (%)
|
64 (58.7)
|
Female, n (%)
|
45 (41.3)
|
Onset age, median (range)
|
4 years (1 month 17 days to 14 years)
|
Infant, n (%)
|
17 (15.6)
|
1–3 years, n (%)
|
45 (41.3)
|
4–6 years, n (%)
|
23 (21.1)
|
7–15 years, n (%)
|
24 (22)
|
Follow-up, median (range)
|
6.5 years (1 to 15 years)
|
Sub-type, n (%)
|
Caudate head
|
38 (34.9)
|
Thalamus
|
21 (19.2)
|
Lenticular nucleus
|
50 (45.9)
|
Symptom, n (%)
|
Hemiplegia
|
107 (98.2)
|
Facioplegia
|
46 (42.2)
|
Aphasia
|
27 (24.8)
|
Seizures
|
18 (16.5)
|
Headache/vomiting
|
9 (8.3)
|
Aetiology, n (%)
|
Mild trauma
|
53 (48.6)
|
Bilateral basal ganglia calcification
|
21 (19.3)
|
Increased homocysteine
|
8 (7.3)
|
Vasculitis
|
4 (3.7)
|
Infection
|
4 (3.7)
|
Congenital vascular malformation
|
5 (4.6)
|
Cardiac disease
|
5 (4.6)
|
Cardiac interventional surgery
|
2 (1.8)
|
Atrial myxoma
|
2 (1.8)
|
Tetralogy of Fallot
|
1 (0.9)
|
Unknown
|
17 (15.6)
|