From: Pain in adult myotonic dystrophy type 1: relation to function and gender
Characteristics | Mean, SD, (Range) | Men (n 24) | Women (n 26) | Difference between men and women/Cohens d |
---|---|---|---|---|
Age, years | 40.1, SD: 12.6. (19–63) | 37, SD: 13.8 (19–63) | 43, SD: 10.7 (23–62) | ns |
CTG kb N49 | 1.8, SD: 1.4 (0.230–5.4) | 1.3, SD: 1.1 (0.270–4.7) n24 | 2.3, SD: 1.5 (0.230–5.4) n25 | P = 0.008/0.8 |
Disease duration, years | 19.0, SD: 10.0 (5–42) | 16.4, SD: 9.6 (5–42) | 21.5, SD: 9.7 (6–40) | ns |
Mean strength of trunk muscles (MTT 0–3) | 1.7, SD: 0.5 (1–2.6) | 1.8, SD: 0.5 (1–2.6) | 1.6, SD: 0.4 (1–2.3) | ns |
Mean strength of distal extremity (MTT 0–3) | 2.3, SD: 0.5 (1.5–3) | 2.3, SD: 0.5 (1.5–3) | 2.3, SD: 0.5 (1.5–3) | ns |
Mean strength of proximal extremity (MTT 0–3) | 2.6, SD: 0.3 (2–3) | 2.7, SD: 0.3 (2–3) | 2.6, SD: 0.3 (2–3) | ns |
Fatigue (FSS) Questionnaire N48 | 4.8, SD: 1.3 (2–7) | 4.5, SD: 1.6 (2–7) n23 | 4.9, SD: 1 (3–7) n25 | Ns / 0.33 |
Walking test (6MWT) N45 | 382.4 SD:117.6 (123–615) | 417.5, SD:103.4 (123–523) n23 | 348.8, SD:122.8 (140–615) n22 | p = 0.049/0.60 |
Katz ADL Questionnaire | [6.0] (3–6) | [5.5] (3–6) | [6.0] (4–6) | ns |
Autism quotient index (AQ) Questionnaire N47 | 17.0, SD: 6.1 (6–32) | 19.4, SD: 5.4 (11–32) n21 | 15.0, SD: 6.1 (6–28) n 26 | p = 0.014 / 0.75 |
IQ N41 | 92.0, SD: 14.2 (64–137) | 92.5, SD:17 (64–137) n20 | 91.5, SD: 11.4 (71–114) n21 | ns/ 0.06 |
Anxiety (BAI) Questionnaire N43 | [4.0] (0–26) | [3.0] (0–26) n22 | [4.5] (0–23) n 22 | ns |
Depression (BDI) Questionnaire N44 | [8.0] (0–37) | [7.0] (0–19) n21 | [8.0] (0–37) n 23 | ns |
Respiration spirometry (FVC%) N 29 | 71.7, SD: 18.8 (25–103) | 76.4, SD: 14.0 (55–103) n13 | 67.9, SD: 21.6 (25–99) n16 | ns/ 0.77 |
Quality of life (WHO QOL BREF) Questionnaire | 89.7, SD: 13.3 (59–115) | 91.3, SD: 12.4 (71–115) n24 | 88.2, SD:14.1 (59–114) n26 | ns/ 0.23 |
BMI | 26.6, SD: 6.6 (15–53) | 26.3, SD: 5.5 (15–34) | 26.9, SD: 7.5 (17–53) | ns/0.09 |