Cranial nerve involved | Shibuya et al 132 cases [3] | Rotta et al 87 cases [8] | Barohn et al 60 cases [9] | McCombe et al 92 cases [10] | Gorson et al 67 cases [11] |
---|---|---|---|---|---|
I | 0 | 0 | 0 | 0 | |
II | 1 (1%) | 0 | 0 | 0 | |
Ophthalmoplegia (III, IV or VI) | 7 (5%) | 3 (3%) | 2(3%) | 4(4%) | 2 (3%) |
V | 4 (3%) | 0 | 0 | 0 | |
VII | 11 (8%) | 2 (2%) | 8(13%) | 14(15%) | 7 (10%) |
VIII | 2 (2%) | 0 | 0 | 0 | |
IX, X | 12 (9%) | 1 (1%) | 0 | 6(6%) | 4 (6%) |
XII | 0 | 0 | 0 | 0 | |
Total | 26(20%) | 4 (5%) | 10(17%) | 15(16%) |