Table 2 Summary of neuroimaging features

Features of White matter lesions

Periventricular white matter lesions (%)

29/29 (100%)

Subcortical and deep white matter lesions- frontal (%)

28/29 (96.6%)

Subcortical and deep white matter lesions- parietal (%)

21/29 (72.4%)

Subcortical and deep white matter lesions- occipital (%)

19/29 (65.5%)

Subcortical and deep white matter lesions- temporal (%)

13/29 (44.8%)

Internal capsule (%)

11/29 (37.9%)

External capsule (%)

21/29 (72.4%)

Corpus callosum (%)

27/29 (93.1%)

Infratentorial white matter (%)

13/29 (44.8%)

Corticomedullary junction DWI high intensity (%)

27/31^a (87.1%)

Frontal and external capsule DWI high intensity (%)

11/31 (35.5%)

Grey matter lesion (%)

5/29 (17.2%)

Gd Enhancement (%)

0/10 (0%)

Visual rating scale

GCA (0–3, median)

1

O’Donavan scale (0–3, median)

2

Periventricular white matter (0–6, \(\overline{\mathrm{x}}\pm \mathrm{s }\))

5.1 \(\pm\) 1.8

Deep white matter (0–24, \(\overline{\mathrm{x}}\pm \mathrm{s }\))

16.1 \(\pm\) 7.2

Basal ganglia white matter (0–30, \(\overline{\mathrm{x}}\pm \mathrm{s }\))

1.5 \(\pm\) 2.2

Infratentorial white matter (0–24, \(\overline{\mathrm{x}}\pm \mathrm{s }\))

1.8 \(\pm\) 2.2

White matter total score (0–84, \(\overline{\mathrm{x}}\pm \mathrm{s }\))

24.4 \(\pm\) 11.3