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Table 3 Clinical and affective characteristics of SCA14 affected subjects and intrafamilial controls

From: Cognition is only minimally impaired in Spinocerebellar ataxia type 14 (SCA14): a neuropsychological study of ten Norwegian subjects compared to intrafamilial controls and population norm

  Affected n = 9 Intrafamilial controls n = 10
  Median/Mean (SD) Median/Mean (SD)
SARA 1, at baseline 5.50/5.83 (3.31) 0
SARA 2, at three years follow up 8.50/8.28 (3.62) 0
Disease duration (in years) 10.00/13.00 (8.60) 0
Age at examination (in years) 44.00/37.33 (14.17) 43.5/41.9 (13.9)
Disability stage 1, at baseline 2.00/2.00 (0.50) 0
Disability stage 2, at three years follow up 2.00/2.00 (0.50) 0
Mini-Mental State (MMS) 30.00/29.67 (0.50) 0
Education (in years) 10/10.33 (2.2) 10/10.8 (2.1)
Male: Female 7:2 4:6
  Mean (n = 9) Mean (n = 9)*
SCL-90   
Total 0.33 (0.41) 0.38 (0.21)
Somatization 0.71 (0.80) 0,67 (0.50)
Obsessive-compulsive 0,46 (0.69) 0,70 (0.59)
Interpersonal sensitivity 0.42 (0.43) 0.15 (0.16)
Depression 0.32 (0.48) 0.48 (0.50)
Anxiety 0.20 (0.28) 0.29 (0.25)
Hostility 0.28 (0.49) 0.11 (0.12)
Phobic anxiety 0.25 (0.43) 0.10 (0.14)
Paranoid ideation 0.22 (0.30) 0.17 (0.19)
Psychoticism 0.09 (0.14) 0.03 (0.05)
Extra-scale 0.50 (0.69) 0.83 (0.51)
  1. *n = 9, one control was known to have ADHD and had a total SCL-90 score of 1.94, and was excluded from the analyses as an outlier.