CIDP all | Typical CIDP | Atypical CIDP | HC | |
---|---|---|---|---|
N total | 33 | 16 | 17 | 28 |
sex, female (%) | 12 (36,4) | 10 (62,5) | 2 (11,76) P = 0.004 | 14 (50) |
age (years), mean (SD) | 64,18 (9,94) | 62,50 (11,65) | 65,75 (8,04) | 59,54 (8,94) |
median (range) | 65 (44–82) | 61 (44–82) | 68 (52–80) | 60 (37–77) |
time since diagnosis, years, median (IQR) | 5 (2–8) | 7,5 (2.75–14.25) | 3 (2–7) | n.a. |
CIDP disease activity status –stabile (%) | 26 (85.8) | 14 (87.5) | 12 (70.6) | n.a. |
handedness, right handed (%) | 31/32a (96.8) | 16 (100) | 16 (94) | n.a. |
INCAT ODSS, mean (SD) | 3.4 (1.6) | 4.4 (1.5) | 2.4 (1.0) P = 0.0002 | n.a. |
- arms | 1.4 (0.75) | 2.4 (1.0) | 1.4 (0,96) P = 0.003 | n.a. |
- legs | 1.5 (0.9) | 2 (1.0) | 1.0 (0.001) | n.a. |
MRC, mean (SD) | 71.5 (7.5) | 68.9 (9.9) | 73.0 (5.1) | n.a. |
treatment actually/ever (%) | ||||
- glucosteroids | 7/24 (21/72.8) | 5/13 (31/81) | 2/11 (12/64) | n.a. |
- IVIg | 19/33 (58/100) | 10/16 (63/100) | 9/17 (53/100) | n.a. |
- PE | 0/8 (0/24.2) | 0/4 (0/25) | 0/4 (0/23) | n.a. |
- other | 5/7 (15/21) | 3/5 (19/31) | 2/2 (12/12) | n.a. |