Fig. 2

Ptosis, eye movements, muscle MRI and pathological findings in case 2. On admission, case 2 exhibited bilateral ptosis (Above). After treatment, ptosis was improved (Below) (a). Restriction of eye movements on admission (b). Hyperintense signal and enhancement on short T2 inversion recovery (STIR) in bilateral orbicularis oculi muscle: coronal view (c) posterior cervical muscle (d), and brachial muscle (e). Yellow arrow indicates inflammation change. Muscle biopsy shows muscle fiber necrosis and regeneration with sparse inflammatory infiltrate with hematoxylin and eosin staining. (f, g)