Increased incidence of Susac syndrome: a case series study

BMC Neurology

Table 1 Demographic and clinical presentation

	Time to diagnosis	Disease severity	Lumber Puncture			CNS involvment			Eye involvment		Ear involvment		Complete triad***	Serology	Non-neurological symptoms
			Opening Pressure (mm H2o)	WBC (cells/μl)	Protein (mg/dl)	Cognitive/ Psychiatric	Focal signs	Headache	S*	A-S**	S*	A-S**
1.M/20	Two weeks	Severe	260	1	110	Cognitive + psychiatric	Aphasia and sensory disturbance	+		BL	BL		+	CMV IgM	GI symptoms
2.F/34	Two weeks	Moderate	80	14	125	Moderate encephalopathy	–	–		BL	UL+ Vertigo		+
3.F/20	Three weeks	Mild	–	–	–	Cognitive + psychiatric	–	+	UL				–		GI symptoms
4.F/38	Two weeks	Moderate	165	3	61	Cognitive + psychiatric	–	–	BL			BL	+	CMV IgM	GI symptoms
5.M/35	Nine weeks	Severe	N/A	9	140	Cognitive impairment	–	+	BL		UL		+
6.M/33	Three weeks	extremely severe	205	3	109	Severe encephalopathy	Left hemiparesis	+		BL		BL	+	CMV IgM
7.F/30	Two weeks	Moderate	220	4	99	Cognitive impairment	Left hemihypoesthesia	+	BL		–	–	–	Anti Streptolysin

Note: *S – symptomatic, **A-S – A-symptomatic. *** complete triad – evidence for CNS, retinal and Vestibulocochlear involvement; UN – unilateral, bilateral, Abbreviations: CMV – cytomegalovirus, GI – gastrointestinal, WBC –white blood cells

ISSN: 1471-2377