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Table 1 Clinical features of MuSK MG patients

From: Spotlight on MuSK positive myasthenia gravis: clinical characteristics, treatment and outcomes

Characteristic

Males

(n = 4)

Females

(n = 17)

Total

(n = 21)

Mean age in years (SD)

66.25 ± 8.62

49.24 ± 16.68

52.48 ± 16.75

Mean age at onset in years (SD)

66.00 ± 8.41

48.53 ± 15.86

51.86 ± 16.16

First symptom

 Ocular

2/4

8/17

10/21

 Bulbar

1/4

7/17

8/21

 Neck

0/21

1/21

1/21

 Limb

1/4

1/17

2/21

Clinical subtypes at onset

   

 Ocular

2/4

8/17

10/21

 Generalized

2/4

9/17

11/21

MGFA status at onset

 I

2/4

8/17

10/21

 II

1/4

8/17

9/21

 III

1/4

1/17

2/21

 IV

0/4

0/17

0/21

 V

0/4

0/17

0/21

AChR positive

0/4

1/17

1/21

RNS abnormalities

2/4

14/17

16/21

Thymoma present

0/4

0/17

0/21

Thymectomy

0/4

0/17

0/21

Myasthenic crises

1/4

5/17

6/21

Neostigmine test

3/4

15/17

18/21

Medications at early follow up

 Pyridostigmine bromide

1/4

5/17

6/21

 Corticosteroids

2/4

9/17

11/21

 Tacrolimus

2/4

0/17

2/21

 Azathioprine

0/4

2/17

2/21